IADR Abstract Archives

A Case Report: Osteogenic Changes Following Dentectomy in Fibrous Dysplasia Ossificans Progressiva.

Objectives: Fibrous Dysplasia ossificans progressiva is an extremely rare incurable disorder that results in the abnormal formation of bone outside of the skeleton. It occurs in 1 in every 2million people in a population and is generally noticed in early childhood. A mutation in the ACVR1 gene, an autosomal dominant gene, results in excessive bone formation which occurs all over the body sparing the tongue, diaphragm, extra ocular muscles, cardiac muscle and smooth muscle. In the event of injury, a patient with FOP will heal at the site of injury with more bone formation thus resulting in limitation in mobility.
Methods: Method: The patient had a preoperative CBCT taken. These x rays were compared to 3 month postoperative CBCT. The osteogenics changes in the jaws were scrutinised and documented. These changes ultimately indicated the healing process of a patient with FOP. Images to be included once follow up has completed.
Results: Case presentation: A young white male from south Africa presented to GSH with painful teeth. Patient was referred to the Maxillofacial and oral surgery clinic due to limited mouth opening as a result of TMJ ankylosis.The patient also has a history of FOP which was diagnosed at a younger age. This was to be a challenge as a dentectomy was required. The healing process for this patient will be vastly different due to the accelerated ossification process following extraction. The outcome of this healing process was unpredictable. The extractions were performed under general anaesthesia by Senior Maxillofacial and Oral surgeon Dr G Hein. The procedure was uneventful without complication and was carried out by removing anterior teeth first, followed by posteriors.
Conclusions: Discussion (results\conclusion): Patient is due for a 3 months post operative follow up which will include CBCT radiographs to take place tuesday 12/10/2021

2021 South African Division Meeting (Virtual)
Virtual
2021

Oral & Maxillofacial Surgery Research
  • Thompson, Junaid  ( UWC , Cape town , Western cape , South Africa )
  • none
    Poster Session
    Abstracts Accepted