IADR Abstract Archives
Dental Management of a Patient With Osteogenesis Imperfecta.
Objectives: Osteogenesis imperfecta (OI) refers to a group of connective tissue disorders that affect about 1/13,500-15,000 births worldwide. It is caused by quantitative and qualitative defects of type 1 collagen and non-collagenous matrix proteins and is characterized by bone fragility. It has distinct oral manifestations including microdontia, hypodontia, crown and root defects, delayed eruption, Class III malocclusion and dentinogenesis imperfecta. The aim of this case report is to describe the oral manifestations and dental management of a patient diagnosed with osteogenesis imperfecta.
Methods: A 4-year-old girl with medical history of OI was referred by a general practitioner to the Department of Paediatric Dentistry (NKUA), with “broken and gray teeth”. Initial clinical examination revealed dentinogenesis imperfecta with gray opalescent discoloration of anterior and posterior primary teeth and post-eruptive breakdown, caries, attrition and fusion of teeth # 72-73 and #82- 83. Radiographic examination showed thin and narrowed roots, cervical constriction and agenesis of two lower incisors.
Results: Management of the case involved an individualized preventive program for high caries risk patients every 4 months, and restorative treatment of anterior teeth with composite resin and posterior teeth with stainless steel crowns. One year post-treatment oral hygiene was improved and there were no new caries or fractures detected.
Conclusions: The goals of treatment for these patients are removal of infection, restoration of aesthetics and protection of posterior teeth from attrition. Individualized treatment varies according to the age of the patient and the severity of the defects and close monitoring with long-term follow-up is necessary.
Methods: A 4-year-old girl with medical history of OI was referred by a general practitioner to the Department of Paediatric Dentistry (NKUA), with “broken and gray teeth”. Initial clinical examination revealed dentinogenesis imperfecta with gray opalescent discoloration of anterior and posterior primary teeth and post-eruptive breakdown, caries, attrition and fusion of teeth # 72-73 and #82- 83. Radiographic examination showed thin and narrowed roots, cervical constriction and agenesis of two lower incisors.
Results: Management of the case involved an individualized preventive program for high caries risk patients every 4 months, and restorative treatment of anterior teeth with composite resin and posterior teeth with stainless steel crowns. One year post-treatment oral hygiene was improved and there were no new caries or fractures detected.
Conclusions: The goals of treatment for these patients are removal of infection, restoration of aesthetics and protection of posterior teeth from attrition. Individualized treatment varies according to the age of the patient and the severity of the defects and close monitoring with long-term follow-up is necessary.